Juvenile pityriasis rubra pilaris. A case report treated with etanercept




Víctor M. Gutiérrez-San Lucas, Servicio de Dermatología, Hospital de Especialidades “Teodoro Maldonado Carbo”, Guayaquil, Ecuador
Isabel Talledo-Mera, Servicio de Dermatología, Hospital de Especialidades “Teodoro Maldonado Carbo”, Guayaquil, Ecuador
Ingrid de los Ángeles Masson-Pinto, Servicio de Dermatología, Hospital de Especialidades “Teodoro Maldonado Carbo”, Guayaquil, Ecuador
Johana M. Romo-Erazo, Servicio de Dermatología, Hospital de Especialidades “Teodoro Maldonado Carbo”, Guayaquil, Ecuador
Carmen López-Acosta, Servicio de Dermatología, Hospital de Especialidades “Teodoro Maldonado Carbo”, Guayaquil, Ecuador


Pityriasis rubra pilaris is a rare skin disease whose etiology is unknown, characterized by hyperkeratotic follicular papules, scaly plaques that can progress to erythroderma, with islands of sparing, and palmoplantar keratoderma. Subtypes III, IV, and V according to the classification of Griffiths, are observed exclusively in children. The treatment of this dermatosis constitutes a challenge, there is no universally accepted treatment since the response rate to different therapies varies widely. We present the case of a type III juvenile pityriasis rubra with a good response to etanercept.



Keywords: Pityriasis rubra pilaris. Juvenile. Treatment. Etanercept.