Oral manifestations in Parry-Romberg syndrome

Joaquín Cotella, División de Dermatología, Hospital General de Agudos J.M. Ramos Mejía, Ciudad Autónoma de Buenos Aires, Argentina
Sabrina Merenzon, División de Dermatología, Hospital General de Agudos J.M. Ramos Mejía, Ciudad Autónoma de Buenos Aires, Argentina
Lola Kuperman-Wilder, División de Dermatología, Hospital General de Agudos J.M. Ramos Mejía, Ciudad Autónoma de Buenos Aires, Argentina
Luciana Cabral-Campana, División de Dermatología, Hospital General de Agudos J.M. Ramos Mejía, Ciudad Autónoma de Buenos Aires, Argentina
Gabriela Bendjuia, División de Dermatología, Hospital General de Agudos J.M. Ramos Mejía, Ciudad Autónoma de Buenos Aires, Argentina

The Parry-Romberg syndrome is a rare subtype of linear cephalic morphea that poses a challenge for the medical team. It primarily affects the area innervated by the trigeminal nerve, resulting in unilateral facial atrophy. Cutaneous manifestations and oral involvement can coexist in approximately 26-47% of cases. Early treatment during the inflammatory stage prevents progression to fibrotic stages. Here, we present a series of three clinical cases with diverse oral manifestations, their treatment response, and their longitudinal management.

Keywords: Morphea. Progressive hemifacial atrophy. Progressive facial hemiatrophy. Parry-Romberg Syndrome. Oral manifestations.