Francisco J. Melgosa-Ramos, Servicio de Dermatología, Hospital Universitario Doctor Peset. Valencia, España
Andrea Estébanez-Corrales, Servicio de Dermatología, Hospital Universitario Doctor Peset. Valencia, España
Enrique Salmerón-González, Servicio de Cirugía Plástica, estética y reparadora, Valencia, España
Encarna Martí-Ibor, Servicio de Anatomía Patológica. Hospital Universitario Doctor Peset. Valencia, España
Eva M. Sánchez-Martínez, Servicio de Dermatología, Hospital Universitario Doctor Peset de Valencia, Valencia, España
Almudena Mateu-Puchades, Servicio de Dermatología, Hospital Universitario Doctor Peset de Valencia, Valencia, España
Cutaneous leiomyosarcoma is an uncommon malignant neoplasm that represents less than 0.05% of skin tumors, much less frequent than other sarcomas such as Kaposi sarcoma or dermatofibrosarcoma protuberans. Three main subtypes are distinguished with different management and prognosis: dermal leiomyosarcoma, subcutaneous leiomyosarcoma, and metastatic leiomyosarcoma. Despite its simplicity, this classification does not always allow to classify a LMSC as dermal or subcutaneous, causing certain variability in some aspects such as the extension study, surgical management, and the adjuvant therapy. In addition, the low prevalence of these tumors does not help to achieve standardized management on daily clinical practice. We present a case of LMSC that allows us to discuss the questions raised.
Keywords: Cutaneous Leiomyosarcoma. Dermal Leiomyosarcoma. Leiomyosarcoma treatment.